Skull Base 2004; 14(2): 109-113
DOI: 10.1055/s-2004-828705
CASE REPORT

Copyright © 2004 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA.

Malignant Peripheral Nerve Sheath Tumor of the Orbit: Case Report and Literature Review

Mehmet D. Aydin1 , Umran Yildirim2 , Cemal Gundogdu2 , Osman Dursun3 , Hasan H. Uysal3 , Mete Ozdikici4
  • 1Department of Neurosurgery, Medical Faculty, Ataturk University, Erzurum, Turkey
  • 2Department of Pathology, Medical Faculty, Ataturk University, Erzurum, Turkey
  • 3Department of Ophthalmology, Social Security Hospital, Erzurum, Turkey
  • 4Department of Radiology, Erzurum State Hospital, Erzurum, Turkey
Further Information

Publication History

Publication Date:
04 June 2004 (online)

A 68-year-old woman with progressive visual loss and exophthalmos in her right eye had been operated on for a mass in her right calf 3 years earlier. Imaging showed a huge mass invading the orbital structures and temporal pole. The presumptive diagnosis was a malignant orbital tumor. The tumor was resected totally and eroded tissues such as the lateral rectus muscle and dural compartments were repaired. The histological diagnosis was a malignant peripheral nerve sheath tumor (MPNST). The patient recovered uneventfully and was discharged 8 days after surgery. Two years later she died from a liver tumor. Few MPNSTs involving the orbit have been reported.

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 Dr
Mehmet D Aydin

Atatürk Üniversitesi Lojmanlari

60 Blok, Kat 1, No. 3, Erzurum, Turkey

Email: nmda21@hotmail.com

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