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Rhabdomyosarcoma of nose, nasopharynx and paranasal sinuses

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Indian Journal of Otolaryngology and Head & Neck Surgery Aims and scope Submit manuscript

Abstract

Rhabdomyosarcoma is an aggressive malignant soft tissue tumor that arises from primitive striated muscle cells called rhabdomyoblasts. It is the most common soft tissue malignant tumor in children and accounts for about 7–8% of childhood cancers. It can arise from almost anywhere in the body but it is most common in the head and neck region. This article presents six cases of rhabdomyosarcoma involving the nose, nasopharynx and the paranasal sinuses four of which were treated with a combination of radiotherapy and chemotherapy and two were treated with medial maxillectomy combined with chemotherapy and radiotherapy.

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References

  1. Womer RB, Pressey JG (2000) Rhabdomyosarcoma and soft tissue sarcoma in childhood. Current Opin Oncol 12:337–344

    Article  CAS  Google Scholar 

  2. Maurer HM (1984) Clinical Pediatric Oncology, Mosby-Year Book, St. Louis, MO

    Google Scholar 

  3. Dito WR, Batsakis JG (1962) Rhabdomyosarcoma of head and neck; Appraisal of biologic behaviour in 170 cases. Arch Surg 84:582

    CAS  PubMed  Google Scholar 

  4. Mason JK, Soule EH (1965):Embryonal Rhabdomyosarcoma of head and neck; American Journal of Surgery, 110, No. 4

  5. Albores-Saovedra I, Martin RG & Smith JL Jr.: Rhabdomyosarcoma; A study of 35 cases. Annals of Surgery

  6. Sercarz JA, Mark RJ, Tran L, Storper I, et al (1994) Sarcomas of the nasal cavity and paranasal sinuses. Ann Otol Rhinol Laryngol 103:699–704

    CAS  PubMed  Google Scholar 

  7. Tapscott SJ, Weintraub H (1991) MyoD and the regulation of myogenesis by helix-loop-helix proteins: J Clin Invest 87:1133–1138

    Article  CAS  PubMed  Google Scholar 

  8. Tsokos M (1994) The diagnosis and classification of childhood rhabdomyosarcoma. Semin Diagn Pathol 11: 26–38

    CAS  PubMed  Google Scholar 

  9. Pappo AS, Shapiro DN, Crist WM, et al (1995) Rhabdomyosarcoma, biology and treatment. J Clin Oncol 13:2123–2129

    CAS  PubMed  Google Scholar 

  10. Horne RC Jr. & Enterline HF (1958); Rhabdomyosarcoma: A clinicopathological study and classification of 39 cases; Cancer, 11:181.

    Article  Google Scholar 

  11. Suton Wutaru W & Montague Eleanor D (1967): Paediatric Tumours-Cancers of the head and neck; edited by Mac Comb WS & Fletcher GH; Williams Wilkins & Co. Baltimore

    Google Scholar 

  12. Yao-Shi Fu & Perzin KH (1976): Non-epithelial tumours of the nasal cavity, paranasal sinuses and nasopharynx. Clinicopathological study of skeletal muscle tumours (Rhabdomyoma and rhabdomyosarcoma); Cancer 37: 364–376

    Article  Google Scholar 

  13. Crist W, Gehan EA, Ragab AH, et al (1995) The Third Intergroup Rhabdomyosarcoma Study. J Clin Oncol 13: 610–630

    CAS  PubMed  Google Scholar 

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Correspondence to Prabir Kumar Mondal.

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Mondal, P.K., Pal, I., Misra, S. et al. Rhabdomyosarcoma of nose, nasopharynx and paranasal sinuses. Indian J Otolaryngol Head Neck Surg 61, 317–319 (2009). https://doi.org/10.1007/s12070-009-0090-9

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  • DOI: https://doi.org/10.1007/s12070-009-0090-9

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