RT Journal Article SR Electronic T1 Ewing's Sarcoma Family Tumors in the Jaws: Case Report, Immunohistochemical Analysis and Literature Review JF In Vivo JO In Vivo FD International Institute of Anticancer Research SP 481 OP 491 VO 31 IS 3 A1 ANA REGINA CASAROTO A1 MARCELO BONIFACIO DA SILVA SAMPIERI A1 CLEVERSON TEIXEIRA SOARES A1 PAULO SERGIO DA SILVA SANTOS A1 RENATO YASSUTAKA FARIA YAEDU A1 JOSÉ HUMBERTO DAMANTE A1 VANESSA SOARES LARA YR 2017 UL http://iv.iiarjournals.org/content/31/3/481.abstract AB Due to the low incidence of the Ewing's Sarcoma (ES) family tumors, the available epidemiology is likely to be unreliable, and at present, there are no standard diagnostic or clinical guidelines outlining their management. This report describes a case of peripheral primitive neuroectodermal tumor (ES/pPNET) which initially mimicked cystic lesions, and describes a comparison between ES and ES/pPNET in the jaws by the World Health Organization classification. This review addressed 63 cases published in the English literature between 1950 and 2016. The majority of cases were ES. Both ES and ES/pPNET mimicked other benign entities such as traumatic, cystic and inflammatory lesions. The patients who died of their disease had a history of metastatic tumors, and primary tumor located in the mandible and maxilla for ES and ES/pPNET, respectively. The differentiation of the ES family tumors from other small blue-cell tumors may be difficult and requires familiarity with histological and immunohistochemical features.