RT Journal Article
SR Electronic
T1 Ewing's Sarcoma Family Tumors in the Jaws: Case Report, Immunohistochemical Analysis and Literature Review
JF In Vivo
JO In Vivo
FD International Institute of Anticancer Research
SP 481
OP 491
VO 31
IS 3
A1 CASAROTO, ANA REGINA
A1 DA SILVA SAMPIERI, MARCELO BONIFACIO
A1 SOARES, CLEVERSON TEIXEIRA
A1 DA SILVA SANTOS, PAULO SERGIO
A1 YAEDU, RENATO YASSUTAKA FARIA
A1 DAMANTE, JOSÉ HUMBERTO
A1 LARA, VANESSA SOARES
YR 2017
UL http://iv.iiarjournals.org/content/31/3/481.abstract
AB Due to the low incidence of the Ewing's Sarcoma (ES) family tumors, the available epidemiology is likely to be unreliable, and at present, there are no standard diagnostic or clinical guidelines outlining their management. This report describes a case of peripheral primitive neuroectodermal tumor (ES/pPNET) which initially mimicked cystic lesions, and describes a comparison between ES and ES/pPNET in the jaws by the World Health Organization classification. This review addressed 63 cases published in the English literature between 1950 and 2016. The majority of cases were ES. Both ES and ES/pPNET mimicked other benign entities such as traumatic, cystic and inflammatory lesions. The patients who died of their disease had a history of metastatic tumors, and primary tumor located in the mandible and maxilla for ES and ES/pPNET, respectively. The differentiation of the ES family tumors from other small blue-cell tumors may be difficult and requires familiarity with histological and immunohistochemical features.